What is Ewing sarcoma?

Ewing sarcoma is a malignant tumor that primarily develops in the bones, affecting mainly long bones, flat bones, and the axial skeleton. The tumor may be localized or metastatic, especially to the lungs or bones/bone marrow.

In France, about 80 to 100 cases of Ewing sarcoma¹ are diagnosed each year, with a peak incidence during adolescence and among young adults. It occurs mainly in Caucasian populations, much less frequently in African or Asian populations, and affects males slightly more often than females (ratio of 3:2).

Risk factors for Ewing sarcoma

Despite its marked predominance among Caucasians, no environmental or genetic risk factors have been clearly identified for Ewing sarcoma.

[1]French Society for Childhood and Adolescent Cancer and Leukemia (SFCE) Malignant primary bone tumors - SFCE